From: IgG4- related disease: an orphan disease with many faces
Pancreas | IgG4-related pancreatitis (Type 1 autoimmune pancreatitis) |
Bile ducts, gallbladder and liver | IgG4-related sclerosing cholangitis |
 | IgG4-related cholecystitis |
 | IgG4-related hepatopathy |
Thyroid gland | IgG4-related thyroid disease |
Salivary and lacrimal glands | IgG4-related sialadenitis |
 | IgG4-related parotitis |
 | IgG4-related submandibular gland disease |
 | IgG4-related dacryoadenitis |
Orbits | IgG4-related ophthalmic disease |
 | IgG4-related orbital inflammatory pseudotumor |
 | IgG4-related pan-orbital inflammation |
 | IgG4-related orbital myositis |
Retroperitoneal fibrosis, arteries | IgG4-related retroperitoneal fibrosis |
 | IgG4-related aortitis/periaortitis |
 | IgG4-related periarteritis |
Intrapulmonary, mediastinal and pleural involvement | IgG4-related lung disease |
 | IgG4-related mediastinitis |
 | IgG4-related pleuritis |
Lymph nodes | IgG4-related lymphadenopathy |
Kidney | IgG4-related kidney disease |
 | tubulointerstitial nephritis secondary to IgG4-related disease |
 | membranous glomerulonephritis secondary to IgG4-related disease |
 | IgG4-related renal pyelitis |
Miscellaneous | IgG4-related perineural disease* |
 | IgG4-related pachymeningitis |
 | IgG4-related hypophysitis |
 | IgG4-related mesenteritis |
 | IgG4-related mastitis |
 | IgG4-related prostatitis |
 | IgG4-related epididymo-orchitis* |
 | IgG4-related paratesticular pseudotumor* |
 | IgG4-related skin disease |
 | IgG4-related pericarditis |