Table 1 Frequency of ocular findings in the National EB Registry study population by EB subtype (%)
From: A review of scoring systems for ocular involvement in chronic cutaneous bullous diseases
| Â | EB Simplex | Junctional EB | Dystrophic EB | |||||||
|---|---|---|---|---|---|---|---|---|---|---|
Manifestation | Localised (N = 1092) | G-S (N = 113) | G-I (N-96) | Ogna (N = 379) | G-S (N = 40) | G-I (N = 190) | DDEB G (N = 424 | RDEB G-S (N = 139) | RDEB G-I (N = 265) | RDEB Inversa (N = 17) |
Corneal erosions/blisters | 0.92 | 6.19 | 3.13 | 2.64 | 47.50 | 25.26 | 2.12 | 74.10 | 32.45 | 35.29 |
Corneal scarring | 0.27 | 0.00 | 3.16 | 0.53 | 26.83 | 13.37 | 0.95 | 50.00 | 16.92 | 29.41 |
Symblepharon | 0.00 | 0.00 | 0.00 | 0.00 | 4.76 | 2.11 | 0.00 | 10.07 | 1.89 | 11.76 |
Blepharitis | 0.37 | 0.88 | 2.08 | 0.26 | 7.14 | 6.32 | 0.71 | 17.52 | 6.46 | 17.65 |
Ectropion | 0.00 | 0.00 | 0.00 | 0.00 | 14.29 | 2.11 | 0.00 | 7.19 | 1.90 | 0.00 |
Lacrimal duct obstruction | 1.19 | 2.65 | 1.04 | 1.85 | 2.38 | 4.23 | 1.65 | 5.80 | 5.30 | 11.76 |
Impaired vision | 13.17 | 13.27 | 15.63 | 16.14 | 16.67 | 13.68 | 17.18 | 38.13 | 21.89 | 41.18 |
Blindness | 0.82 | 1.77 | 0.00 | 0.53 | 0.00 | 1.58 | 0.94 | 6.47 | 1.14 | 0.00 |