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Table 2 The provisional classification crieria for pediatric Behçet's disease

From: French recommendations for the management of Behçet’s disease

Item

Description

Value/item

Recurrent oral aphthosis

At least 3 episodes/year

1

Ulceration or genital aphthosis

Typical with scarring

1

Cutaneous damage

Necrotic folliculitis

Acneiform lesions

Erythema nodosum

1

Ocular damage

Anterior uveitis

Posterior uveitis

Retinal vasculitis

1

Neurological signs

With the exception of isolated headaches

1

Vascular signs

Venous thromboses

Arterial thromboses

Arterial aneurysms

1