From: Pancreatic involvement in patients with inborn errors of metabolism
 | Age (years) | Number of hospitalizations | Precipitating factors | Pancreatic disorders |
---|---|---|---|---|
MMA (Case 1) | 15 16 19 20 | 1 3 2 1 | Dehydration, fever, poor oral intake, liver dysfunction | Pancreatitis, Diabetes, Mellitus |
MMA (Case 2) | 21 | 1 | Respiratory infection, weight loss, bronchial, asthma, vomiting, dehydration | Pancreatitis, Diabetes |
PPA (Case 3) | 14 | 1 | Diabetes mellitus for 14Â years | Diabetes |
PPA (Case 4) | 4 5 6 8 | 1 2 1 1 | Surgery for intestinal obstruction, swine flu, fever, dehydration, ferritinemia | Pancreatitis, Diabetes |
FAO (Case 5) | 10 | 1 | Fasting, dehydration | Pancreatitis |
Ornithine (Case 6) | 33 | None | No diet control for ornithine | Diabetes |