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Table 5 Treatment and clinical data at last follow-up

From: Phenotypic characterization of X-linked hypophosphatemia in pediatric Spanish population

Patient

Phosphorus element dose (mg/kg/day)

Vitamin D dose (µg/day)

Nephrocalcinosis

I.1

38a

0.50c

No

I.2

40a

0.50c

No

II.1

86a

1.20d

Yes

III.1

IV.1

83a

0.60d

No

IV.2

62a

1.00d

No

V.1

VI.1

VII.1

No

VII.2

VII.3

55b

0.50c

Yes

VII.4

52b

0.50c

Yes

VIII.1

90a

1.50d

Yes

IX.1

X.1

40a

0.25d

No

XI.1

83a

0.50c

No

XII.1

44b

0.29d

No

XIII.1

41b

0.25c

Yes

XIV.1

52a

1.20d

XV.1

41b

1.00c

No

XVI.1

XVII.1

45b

0.25c

Yes

XVIII.1

XIX.1

27b

0.50c

Yes

XX.1

32a

0.50c

No

XXI.1

63a

1.50d

No

XXII.1

XXIII.1

65a

1.10d

No

XXIV.1

XXV.1

38a

1.40c

XXVI.1

58b

0.25c

No

XXVII.1

48b

0.60d

No

XXVII.2

XXVIII.1

XXVIII.2

XXIX.1

0.10d

No

XXX.1

XXX.2

Yes

XXXI.1

XXXII.1

XXXIII.1

49b

0.75c

No

XXXIV.1

XXXV.1

XXXV.2

XXXVI.1

XXXVII.1

XXXVIII.1

XXXIX.1

  1. aPhosphate was administered as a solution
  2. bPhosphate was administered as tablets
  3. cCorresponds to 1,25 dihydroxy vitamin D
  4. dCorresponds to 1 hydroxy vitamin D