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Fig. 1 | Orphanet Journal of Rare Diseases

Fig. 1

From: Sirolimus in the treatment of kaposiform lymphangiomatosis

Fig. 1

Patient 1 showed a grossly distended abdomen and perineal ecchymosis (A). Axial T2 fat-saturated image showed extensive mediastinal involvement (B). Coronal T2 fat-saturated image showed extensive abdominal cavity and pelvic cavity involvement (C). Axial T2 fat-saturated image showed bilateral inguinal regions, including testis involvement (D)

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