Fig. 1From: Sirolimus in the treatment of kaposiform lymphangiomatosisPatient 1 showed a grossly distended abdomen and perineal ecchymosis (A). Axial T2 fat-saturated image showed extensive mediastinal involvement (B). Coronal T2 fat-saturated image showed extensive abdominal cavity and pelvic cavity involvement (C). Axial T2 fat-saturated image showed bilateral inguinal regions, including testis involvement (D)Back to article page