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Table 1 Results from the literature analyses

From: The combined prevalence of classified rare rheumatic diseases is almost double that of ankylosing spondylitis

Classification

N = 

Combined prevalence/100.000

%/All RD (prevalence)

Vasculitis

15

76.8

26.55

Arthritis

11

89.3

30.9

Autoinflammatory

11

21.105

7.32

Bone disorders

11

4.15

1.44

Myositis

9

19.5

6.76

Connective tissue disease

8

46.1

15.99

Others

8

30.89

10.72

Overgrowth syndromes

3

0.3

0.1

Total

76

288.15

100