From: Functional mobility in walking adult population with ataxia of Charlevoix-Saguenay
Characteristic | Total group n = 35 | No walking aid n = 19 | Walking aid n = 16 | p-value* |
---|---|---|---|---|
Age, (y) | ||||
Mean (SD) | 32.2 (10.4) | 26.5 (7.6) | 38.9 (9.4) | < 0.001 |
Range | 16–65 | 16–42 | 25–65 | |
Sex, n (%) | ||||
Men | 15 (42.9) | 11 (73.3) | 4 (26.7) | 0.087 |
Women | 20 (57.1) | 8 (40.0) | 12 (60.0) | |
Age groups, n (%) | ||||
16–29 | 14 (40.0) | 13 (92.9) | 1 (7.1) | |
30–39 | 16 (45.7) | 5 (11.0) | 11 (68.8) | – |
≥ 40 | 5 (14.3) | 1 (20.0) | 4 (80.0) | |
Falls (period) | ||||
6 months | ||||
Mean (SD) | 8.8 (11.1) | 11.1 (13.5) | 6.3 (7.3) | 0.219 |
Range | 0–50 | 0–50 | 0–26 | |
1 year | ||||
Mean (SD) | 17.6 (22.1) | 21.6 (26.9) | 13.0 (14.4) | 0.262 |
Range | 0–100 | 0–100 | 0–52 | |
Disease severity | ||||
DSI-ARSACS (/38) | ||||
Mean (SD) | 13.5 (4.3) | 10.8 | 16.7 | < 0.001 |
Range | 4.5–22.0 | 4.5–16.0 | 11.0–22.0 | |
SARA (/40) | ||||
Mean (SD) | 13.4 (5.9) | 9.2 (4.0) | 18.5 (3.0) | < 0.001 |
Range | 4.0–22.5 | 4.0–20.0 | 11.0–22.5 |